7 results
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Clinical Presentation ... Fever is the main clinical ... Increased soluble IL-2 ... #Diagnosis #Management ... #Hematology #Rheumatology
Hepatopulmonary Syndrome - Diagnosis and Management Summary
A defect in arterial oxygenation due to a gas exchange
Hepatopulmonary Syndrome ... anatomic shunt (Type 2) ... Clinical Presentation ... cirrhosis • Intra-pulmonary ... hepatopulmonary #syndrome
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Primary (essential) 2. ... Cryofibrinogenemia Clinical ... thrombophlebitis, pulmonary ... Diagnosis: • + Clinical ... Antiphospholipid syndrome
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
• Cytopenia: 2% ... salivary ducts Clinical ... : • 10%-15% Pulmonary ... Lymphoma, Cytopenia: 2% ... Rheumatology #Diagnosis #Management
Immune Reconstitution Inflammatory Syndrome - Overview of IRIS

What Is IRIS?
	• A state of hyperinflammatory response that
Reconstitution Inflammatory Syndrome ... worsening of that disease ... the first 1 to 2 ... starting ART < 2 ... Differential #Diagnosis #Management
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
Capillary leak syndrome ... Relapsing-remitting course +++ Clinical ... leukocytosis 2. ... filling +++ (risk of pulmonary ... #diagnosis #management
Pyoderma Gangrenosum (PG)
50 M Crohn’s dz had a small pustule on the ankle 4 mo ago
wide variety of clinical ... Management of PG ... Improvement in 2- ... Gangrenosum #PG #clinical ... #photo #dermatology