4 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
coronary artery aneurysms ... Diagnosis: • Genital ... Arthritis, AS Treatment ... • Nonsurgical abdominal ... Glucocorticoids 5-ASA
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- GI tract: abdominal ... < 30 years - Aorta ... VASCULITIS: • Behçet ... aortitis, aortic aneurysm ... Supply gut -> abdominal
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
< 30 years • Aorta ... Arteritis): • Aorta ... gut involvement, abdominal ... vasculitis • Behcet ... Thrombosis and arterial aneurysms
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
Large vessels (aorta ... other large vessel aneurysms ... Sarcoidosis • Behcet ... disease • Infections ... affected tissue Treatment