4 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
and diplopia) • Vascular ... Disease: Arterial ... coronary artery aneurysms ... Arthritis, AS Treatment ... diagnosis #management #signs
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
< 30 years - Aorta ... VASCULITIS: • Behçet ... Thrombosis and arterial ... aneurysms can also ... purpura: strong sign
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
purpura: Strong sign ... < 30 years • Aorta ... pulse deficits vascular ... vasculitis • Behcet ... aneurysms can also
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
Large vessels (aorta ... other large vessel aneurysms ... Sarcoidosis • Behcet ... ○ Fungal ○ Bacterial ... affected tissue Treatment