6 results
Aortic Dissection Pearls
Aortic dissection is caused by a tear in the tunica intima, the innermost layer
the wall of the aorta ... • Aortic valve disease ... Thoracic aortic aneurysm ... deficit • Shock Treatment ... diagnosis #management #vascular
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Epidemiology: • Young adults ... and diplopia) • Vascular ... coronary artery aneurysms ... Arthritis, AS Treatment ... signs #symptoms #rheumatology
Adult Onset Still's Disease
Systemic inflammation with urticarial rash.
Rash: 
 • Nonpruritic, evanescent (correlates with time of
Adult Onset Still's ... A nonpruritic macular ... negative RF and ANA ... Treatment - Mild ... diagnosis #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
< 30 years - Aorta ... branches • GCA: - Aorta ... VASCULITIS: • Behçet ... aortitis, aortic aneurysm ... differential #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
pulse deficits vascular ... Nervous System: • Onset ... vasculitis • Behcet ... Thrombosis and arterial aneurysms ... Differential #Diagnosis #Rheumatology
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
Symptoms: • Sudden onset ... Large vessels (aorta ... other large vessel aneurysms ... Sarcoidosis • Behcet ... affected tissue Treatment