2 results
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
specific) COMMON CLINICAL ... proteinuria • Lungs ... Essential Criteria: Clinical ... complement • Classification ... • First-Line:
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
for bone, skin, lungs ... populations) CLINICAL ... bones ... Birbeck granules (EM ... Histiocytosis #Diagnosis #Management