10 results
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
ILD caused by inhalation ... , Polymyositis-dermatomyositis ... • Idiopathic pulmonary ... #diagnosis #differential ... #pulmonary #causes
ILD of Known Cause - Differential Diagnosis
Exposure:
 • Occupational: Asbestosis, Silicosis, Hypersensitivity, Pneumonitis
 • Treatment Related:
ILD of Known Cause ... - Differential Diagnosis ... Polymyositis, Dermatomyositis ... #lung #disease ... #pulmonary
Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
disease-associated interstitial lung ... DM/PM : dermatomyositis ... #Differential #Comparison ... #Table #Pulmonary ... #Rheumatology #
Diagnostic algorithm for a child or adolescent with suspected pulmonary hypertension. CHD, congenital heart disease; CPET,
Diagnostic algorithm ... , chronic lung disease ... #Diagnosis #Peds ... #Pediatrics #Pulmonary ... #Hypertension #Workup
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
Periorbital heliotrope (blue-purple ... increases and ILD ... anti-NXP2 Abs Lung ... #rheumatology # ... dermatology #diagnosis
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
: ILD (interstitial ... lung disease), ... Scleroderma #SSc #rheumatology ... #diagnosis #signs ... symptoms #testing #workup
Cryptogenic Organizing Pneumonia (COP)

Cryptogenic Organizing Pneumonia Overview:
 • Idiopathic form of organizing pneumonia
 • formerly BOOP
Unknown • 6-7 cases ... Organizing Pneumonia - Diagnosis ... other processes Workup ... strep, HIV • CTD workup ... #ILD #diagnosis
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
• Immunologic Workup ... Discontinuation of causal ... druginduced #lupus #sle #comparison ... #table #rheumatology ... #diagnosis #management
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
Periorbital heliotrope (blue-purple ... Muscle atrophy may cause ... Non-small-cell lung ... : • ILD was diagnosed ... #rheumatology #
Autoimmune Myositis - Differential Diagnosis Framework

Inflammatory Myopathies: Commonly symmetric proximal muscle weakness, no substantial muscle pain
- Differential Diagnosis ... Anti-MDA5 (RP-ILD ... ), dermato-rheumatologic ... statins - probably caused ... Myositis #Myopathy #rheumatology