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Budd Chiari Syndrome (BCS)

Diagnosis
Clinical Manifestations
Causes
Management

By Dr. Hima Veeramachaneni @hima_vee via @EmoryGastroHep

#BCS #BuddChiari #Budd #Chiari #Syndrome #Hepatology
Budd Chiari Syndrome ... BCS #BuddChiari #Budd ... Syndrome #Hepatology #Gastroenterology
Disorders of the Hepatic and Mesenteric Circulation

Platelets in Cirrhosis
Hypercoagulability in Cirrhosis
Bleeding in Cirrhosis
Portal Vein Thrombosis (PVT)
Mesenteric
Thrombosis (MVT) Budd ... Disorders #Hepatology #Gastroenterology
Portal Hypertension Classification by site of vascular obstruction
1) Post-hepatic Post-sinusoidal: Budd-Chiari syndrome
2) Intrahepatic Post-sinusoidal: Veno-occlusive disease
3)
Post-sinusoidal: Budd-Chiari ... Classification #gastroenterology
Chronic Abdominal Pain Causes - Differential Diagnosis Framework

Many patients with chronic abdominal pain have had prior
dysfunction • PSC • Budd-Chiari ... Differential #Diagnosis #gastroenterology
Muddy Brown Granular Casts three ways - Brightfield, Darkfield, Phase Contrast.

Dr. Vipin Varghese @vipvargh

#Muddy #Brown #Granular
Muddy Brown Granular ... Varghese @vipvargh #Muddy
Ascites Differential Diagnosis Table - Serum Ascites Albumin Gradient (SAAG)

SAAG ≥ 1.1:
 • Cirrhosis
 • Portal
thrombosis • Late budd-chiari ... obstruction • Early budd-chiari
Examples of varying granular and granular/waxy mixed casts: 
A: coarse granular/broad-waxy (and surrounding white blood cells);
light granular/muddy ... granular, C and D: muddy
Diagnosis of ascites according to the serum ascites albumin gradient (SAAG)
SAAG ≥ 1.1:
 - Ascitic protein
Cirrhosis, Late Budd-Chiari ... pericarditis, Early Budd-Chiari
Granular & “Muddy Brown” Casts on Urine Microscopy
A. Finely granular cast B. slightly coarser granular cast
Granular & “Muddy ... coarse (c) and muddy
Budd Chiari Syndrome
Hepatic vein obstruction. Can be caused by thrombosis or sometimes a tumour. Can lead
Budd Chiari Syndrome