7 results
Sickle Cell Disease - Pathophysiology of disease and complications 

Due to the deformed shape, HbS induces
- Pathophysiology ... damage leading to calcium ... Calcium influx leads ... #Pathophysiology ... Complications #Hematology
Pseudogout: pathogenesis and clinical findings
 - Idiopathic (vast majority of cases) -> Mechanism unknown
 - Familial
> Clearance of calcium ... mineralization of calcium ... joint (sudden onset ... Pseudogout #CPPD #Disease ... Signs #Symptoms #Pathophysiology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Lymphohistiocytosis (HLH) Pathophysiology ... • Autoimmune diseases ... SLE+++, Adult-onset ... Still disease, ... treatment #summary #rheumatology
CPPD vs Gout

== CPPD == 

Think About CPPD When:
 • Self-limited synovitis after surgery/trauma (> 65
• Underlying disease ... states Pathophysiology ... precipitates with calcium ... • Nocturnal onset ... Gout #Comparison #rheumatology
Blood Transfusion Reactions

Immune Mediated:
 • Febrile Non-Hemolytic Transfusion Reaction (FNHTR): Most common immune reaction to transfusion.
resembles ARDS, onset ... Graft Versus Host Disease ... binds to serum calcium ... Borrellia (Lyme disease ... diagnosis #management #hematology
Blood Product Transfusions One Pager Summary
Type and screen - determines blood type and detects in recipient
resembles ARDS, onset ... Graft Versus Host Disease ... binds to serum calcium ... Borrellia (Lyme disease ... diagnosis #management #hematology
Pseudogout Summary - Calcium Pyrophosphate Deposition Disease (CPPD)

Pathophysiology:
Pyrophosphate produced by chondrocytes likely precipitates with calcium to
Pseudogout Summary - Calcium ... (CPPD) Pathophysiology ... precipitates with calcium ... characterized by sudden onset ... #Rheumatology #