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Cholestatic Liver Disease: Primary Biliary Cirrhosis vs Primary Sclerosing Cholangitis

#pathophysiology #pbc #psc #hepatology #comparison
Disease: Primary Biliary ... Primary Sclerosing Cholangitis
Right Upper Quadrant Pain
Liver:
 - Infectious: Acute viral hepatitis, Liver abscess
 - Non-infectious: hepatitis (Alcohol, Medications),
Budd-Chiari syndrome Biliary ... cholecystitis, Acute cholangitis ... "ascending cholangitis ... "biliary colic")
Summary table of comparison of the difference between primary biliary cholangitis (PBC) and primary sclerosing cholangitis
between primary biliary ... cholangitis (PBC ... primary sclerosing cholangitis
Causes of Severe Acute Liver Injury
 - Ichemic hepatitis
 - Acute biliary obstruction
 - Drug-Induced liver
hepatitis - Acute biliary ... Hemochromatosis - Primary biliary ... cholangitis
Algorithm for the Diagnosis of Primary Biliary Cholangitis (PBC). 

US, ultrasound; MRCP, magnetic resonance cholangiopancreatography; ALP,
Diagnosis of Primary Biliary ... Cholangitis (PBC ... antibodies #Primary #Biliary ... #Cholangitis #PBC
ACUTE CHOLANGITIS
Legend says that Cholangitis was first defined in 1877 by Jean-Martin Charcot, at which time
ACUTE CHOLANGITIS ... Legend says that Cholangitis ... Today, cholangitis ... infection of the biliary ... individuals with biliary
Classification of Jaundice
Unconjugated hyperbilirubinemia (predominantly indirect bilirubin)
 • Increased bilirubin production (eg, hemolytic anemias, hemolytic reactions,
Dysfunction - Biliary ... certain drugs, biliary ... mononucleosis, cholangitis ... , carcinoma of biliary ... duct, sclerosing cholangitis
Gallstone Diseases
1. Asymptomatic Stones 75%
2. Biliary Pain 20%
3. Acute Cholecystitis 10%
4. Mirizzi's Syndrome < 0.1%
5. Cholangitis/
Biliary Pain 20% ... Cholangitis/ Pancreatitis
Hepatomegaly - Differential Diagnosis Algorithm
Malignant
 • Primary Carcinoma
 • Metastases
 • Lymphoma
 • Leukemia
 • Polycythemia
• Bacterial Cholangitis ... Primary Sclerosing Cholangitis ... • Primary Biliary
Important Causes of RUQ and Midline Abdominal Pain - Illness Scripts
PUD, Gastroenteritis, Small bowel obstruction, Appendicitis,
Pancreatitis Biliary ... Cholecystitis, Acute Cholangitis