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Cholestatic Liver Disease: Primary Biliary Cirrhosis vs Primary Sclerosing Cholangitis

#pathophysiology #pbc #psc #hepatology #comparison
Cholestatic Liver ... Primary Sclerosing Cholangitis
Right Upper Quadrant Pain
Liver:
 - Infectious: Acute viral hepatitis, Liver abscess
 - Non-infectious: hepatitis (Alcohol, Medications),
Quadrant Pain Liver ... viral hepatitis, Liver ... cholecystitis, Acute cholangitis ... "ascending cholangitis
Causes of Severe Acute Liver Injury
 - Ichemic hepatitis
 - Acute biliary obstruction
 - Drug-Induced liver
of Severe Acute Liver ... - Drug-Induced liver ... Primary biliary cholangitis
Drug Induced Liver Injury (DILI) - Stepwise Diagnosis Algorithm
DILI suspicion
Features toxic aetiology: Skin involvement, Kidney injury,
Drug Induced Liver ... Alcohol-related liver ... Primary biliary cholangitis ... Primary sclerosing cholangitis ... Consider liver
Hepatomegaly - Differential Diagnosis Algorithm
Malignant
 • Primary Carcinoma
 • Metastases
 • Lymphoma
 • Leukemia
 • Polycythemia
Non-Malignant • Fatty Liver ... • Bacterial Cholangitis ... Primary Sclerosing Cholangitis
Liver Flukes on ERCP
Here are liver flukes (Fasciola hepatica) extracted from the bile duct during ERCP
Liver Flukes on ... ERCP Here are liver ... in a 20F with cholangitis ... intestines and liver ... drkeithsiau #Liver
Causes of Ascites - Differential Diagnosis Algorithm
Portal Hypertension - Prehepatic:
 • Portal vein thrombosis
 • Splenic
disease • Acute liver ... Primary biliary cholangitis ... Primary sclerosing cholangitis
Primary Biliary Cirrhosis (PBC) - Summary

PBC Epidemiology:
 • Female:Male 9:1
 • Common European descent
 • Age:
cholestasis → Cirrhosis/Liver ... or higher • Liver ... nonsuppurative destructive cholangitis ... sclerosis group cholangitis ... Cirrhosis #PBC #cholangitis
Liver Flukes on Endoscopy
Here are liver flukes (Fasciola hepatica) extracted from the bile duct during ERCP
Liver Flukes on ... Endoscopy Here are liver ... in a 20F with cholangitis ... intestines and liver ... drkeithsiau #Liver
The 6 C’s of Primary Sclerosing Cholangitis (PSC)
PSC is a chronic, cholestatic, immune-mediated disease characterized by
Primary Sclerosing Cholangitis ... progression to end-stage liver ... • CHOLANGITIS ... indications for liver ... and end-stage liver