4 results
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Macrophage Activation ... IL-1 and IL-6, leading ... Fever is the main clinical ... nervous system (CNS) dysfunction ... Syndrome #Diagnosis #Management
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
- Organ dysfunction ... progressive organ dysfunction ... specific) COMMON CLINICAL ... • Pancreas: Type ... complement • Classification
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
) Suspect: Clinical ... Skin Disease Classification ... Kikuchi disease • Type-I ... mild cognitive dysfunction ... Chronic B-cell activation
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
Langerhans cells, a type ... : LCH exhibits features ... populations) CLINICAL ... Birbeck granules (EM ... Histiocytosis #Diagnosis #Management