2 results
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
- Organ dysfunction ... • Key Features ... progressive organ dysfunction ... complement • Classification ... IGG4 #Diagnosis #Management
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
various tissues, leading ... : LCH exhibits features ... • Endocrine Dysfunction ... Birbeck granules (EM ... Histiocytosis #Diagnosis #Management