12 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... Uveitis or retinal vasculitis ... test Most Common Clinical ... #Syndrome #disease ... Diagnosis #criteria #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome ... , small-vessel vasculitis ... association • M > F Clinical ... syndrome (Clinical ... signs #symptoms #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
, infections, drug ... nodules, Deep ulcers ... : • Behcet Disease ... • Cogan syndrome ... #dermatology #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
livedo reticularis, ulcers ... : • Behçet Syndrome ... genital aphthous ulcers ... to exclude are infections ... differential #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
to exclude are infections ... • Behcet syndrome ... genital aphthous ulcers ... • Cogan syndrome ... Differential #Diagnosis #Rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Rarely dominate the clinical ... • Goodpasture syndrome ... cell arteritis Infections ... • Fungal infections ... rash #diagnosis #rheumatology
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
, Vasculitis (e.g ... - Behçet's syndrome ... ENT • Oral ulcers ... - SLE, Behçet's ... differential #diagnosis #rheumatology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Purpura - Skin ulcers ... : • Clinical triad ... : HCV infection, ... • Autoimmune diseases ... classification #rheumatology
Vancomycin induced Leukocytoclastic Vasculitis (LCV) of the Hand
70 M vertebral osteomyelitis on vancomycin and cefepime for
antiphospholipid syndrome ... atrial myxoma, Behcet ... syndrome, granulomatosis ... #dermatology #clinical ... #photo
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... Malignancy • Infections ... sensitivity • Painful ulcers ... Diagnosis: • + Clinical ... Antiphospholipid syndrome