40 results
Aplastic Anemia and Bone Marrow Failure Syndromes with Pancytopenia

Fanconi Anemia
Acquired Aplastic Anemia
Dyskeratosis Congenita & Telemore Biology
Syndromes with Pancytopenia ... Fanconi Anemia ... lauraebrown #Pancytopenia
Pancytopenia - Differential Diagnosis

Congenital Diseases:
• GATA2 deficiency
• Fanconi’s anemia
• Wiskott-Aldrich syndrome
• Ribosomopathy or telomeropathy

Cancer:
• Leukemia
• Lymphoma

Inflammatory
Pancytopenia - Differential ... deficiency • Fanconi ... Tickborne illness #Pancytopenia
Aplastic Anemia - Overview

Who?
• M = F
• 3 peaks:	1) Childhood	2) 15-25 years	3) >60 years

What?
• Aplastic anemia
bone marrow + pancytopenia ... repair DNA, as in Fanconi ... • Peripheral Pancytopenia
Pancytopenia - Differential Diagnosis Algorithm

#Pancytopenia #Differential #Diagnosis #Algorithm #hematology
Pancytopenia - Differential ... Diagnosis Algorithm #Pancytopenia
Localization of Renal Tubular Defects
Fanconi Syndrome: Proximal tubule
Bartter Syndrome: Thick ascending loop of Henle
Gitelman Syndrome: Distal
Tubular Defects Fanconi ... Liddle #Syndrome #Fanconi
Pancytopenia - Differential Algorithm / Schema

- Bone Marrow Failure
- Bone Marrow Infiltration
- Sequestration / Destruction

#Pancytopenia #Differential
Pancytopenia - Differential ... Destruction #Pancytopenia
Pancytopenia Framework and Differential Diagnosis

- VA Joint Chiefs @BostonChiefs

#Pancytopenia #Differential #Diagnosis #algorithm #hematology
Pancytopenia Framework ... BostonChiefs #Pancytopenia
Cancer agents and Electrolyte Disorders
 • Hypocalcemia: Cisplatin from Low Mg, Cetuximab- due to low Mg
Axitinib,
: Ifosfamide - Fanconi ... , Ifosfamide - Fanconi ... BRAF inhibitors- fanconi
Causes of Neutropenia with Pancytopenia - Differential Diagnosis Algorithm
Sequestration:
 • Splenomegaly
Marrow Infiltration:
 • Hematologic and non-hematologic
Neutropenia with Pancytopenia ... deficiencies #Pancytopenia
Pancytopenia - Workup and Differential Diagnosis Algorithm
Consumption Disorders
 1. Autoimmune Mediated Pancytopenia
 2. Splenic Sequestration
Peripheral Destruction
Pancytopenia - Workup ... Autoimmune Mediated Pancytopenia ... myelophthisis) #Pancytopenia