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A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
A System for Vasculitides ... Diagnosis #IM #Rheum #Vasculitis ... #Small #Medium ... #Vessel #Size #Classification ... #Differential #Algorithm
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
, medium vessel ... small vessel vasculitis ... Medium vessel vasculitis ... Small vessel vasculitis ... #Classification
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
abnormalities SMALL ... + MPO-ANCA MEDIUM ... pain, infarct • Small ... against MPO • Complement ... #rheumatology #classification
Break down Vasculitis based on vessel size
#Diagnosis #Rheumatology #Differential #Vasculitis #VesselSize #Small #Medium #Large #Classification
Break down Vasculitis ... #Differential #Vasculitis ... #VesselSize #Small ... #Medium #Large ... #Classification
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... of medium vessels ... central nervous system ... small vessels ... disease - systemic
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis: • Systemic ... primary condition MEDIUM ... and infarcts SMALL ... Elevated AST ALT • Hypocomplementemia ... ) • Hypocomplementemic
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
activate the immune system ... • Low serum C4 complement ... • Cutaneous small-vessel ... disorder (e.g. systemic ... diagnosis #types #classification
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
female, asian • Systemic ... false negative (small ... rheumatoid factor), ± hypocomplementemia ... No necrosis, No vasculitis
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome Systemic ... multiple organs, small-vessel ... vasculitis and ... Arterial (MCC-small ... Medium and large
Pediatric Vomiting - Gastrointestinal and Systemic Causes - Differential Diagnosis Algorithm
Hepatobiliary:
 • Acute Hepatitis
 • Acute
Gastrointestinal and Systemic ... Differential Diagnosis Algorithm ... Gastroenteritis • Small ... Thyroid Disease Systemic ... Infection (Otitis Media