2 results
Summary of Coagulation Deficiencies
Inherited:
 • Hemophilia A - Deficiency of Factor VIII
 • Hemophilia B -
of Factor IX Acquired ... RA, SLE), Post-partum ... Acute DIC - Septic shock ... table #comparison #diagnosis ... #hematology #deficiency
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Lymphohistiocytosis (HLH) Pathophysiology ... Purtilo (XLP) Acquired ... Autoimmune diseases: SLE ... management #treatment #summary ... #rheumatology