6 results
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
- Storiform fibrosis ... proteinuria • Lungs ... Criteria: Clinical/radiologic ... mimics excluded MANAGEMENT ... #Management #Rheumatology
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
biliary, renal, lung ... with response to treatment ... + cells" Treatment ... Disease #diagnosis #management ... #rheumatology
Scleroderma Like Conditions - Differential Diagnosis
Eosinophilic Fasciitis:
 - Orange peel induration (peau d'orange) of proximal extremities
the mainstay of treatment ... Nephrogenic Systemic Fibrosis ... Skeletal muscle fibrosis ... Typically seen in long-standing ... paraproteinemia (IgGλ
Severe Heart Failure & Cardiogenic Shock - Management Checklist 
Evaluation 
 - EKG & echocardiography
1 — Treat the lungs ... Consider BiPAP (vS intubation ... (no B-lines on ultrasound ... Revascularization, treatment ... #Management
Polymyalgia Rheumatica (PMR) Diagnosis and Management Summary

WHAT?
 • Polymyalgia rheumatica (PMR) is a common systemic inflammatory
Diagnosis and Management ... universally used, ultrasound ... TREATMENT: • The ... mainstay of treatment ... #Rheumatology
TAFRO

TAFRO syndrome was first described in 2010, standing for:
- Thrombocytopenia
- Anasarca
- Fever
- Reticulin fibrosis
- Organomegaly

TAFRO syndrome
Fever - Reticulin fibrosis ... POEMS syndrome - IGG4 ... Hypoalbuminemia Treatment ... TAFRO #diagnosis #management ... #rheumatology #