2 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
VEXAS (Vacuoles, E1 ... criteria for 1) hematologic ... • UBA1 = major E1 ... including peripheral blood ... NEJM Review: https
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
Sjogren's Syndrome ... PE, Pulmonary amyloidosis ... , PAH Skin: • ... vasculitis: 10%-16% Liver ... Nephrogenic DI Hematologic