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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
PR3-ANCA): • Microscopic ... disease, and ocular ... ulcers, cutaneous, ocular ... Syndrome: - Ocular ... differential #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
(PR3-ANCA)): Microscopic ... disease, and ocular ... ulcers, cutaneous, ocular ... Cogan syndrome: Ocular ... Differential #Diagnosis #Rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... disease 2019 (COVID ... thrombophlebitis, pulmonary ... emboli, and ocular ... Diagnosis: • + Clinical
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
specific) COMMON CLINICAL ... aortitis, mimics vasculitis ... proteinuria • Lungs: Nodules ... /radiologic evidence ... Diagnosis #Management #Rheumatology
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
gland) biopsy • Ocular ... salivary ducts Clinical ... , INC risk PE, Pulmonary ... ) • Cutaneous vasculitis ... Sjogrens #Syndrome #Rheumatology