6 results
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
be any age) Autoimmune ... Hypocomplementemia • Can cause ... Nephrogenic DI Hematologic ... MALT Lymphoma • Lung ... #Diagnosis #Management
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
• Chronic lung ... Granulomatous lymphocytic interstitial ... lung disease (GLILD ... DDX - Other causes ... hypogammaglobulinemia #immunology #hematology
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
OnePager Summary Autoimmune ... (UPC) ratio • Cardiac ... Goodpasture's cause ... sparing of the lung ... differential #diagnosis #management
Heart failure with Reduced Ejection Fraction (HFrEF)
Clinical Presentation
1. Typical symptoms: dyspnea, orthopnea paroxysmal noctumal dyspnea, fatigue,
: weight gain, lung ... Chest x-ray: signs ... → no signs of CXR ... Consider cardiac ... heartfailure #diagnosis #management
Congestive heart failure (CHF) is the result of insufficient output because of cardiac failure, high resistance
In the lungs LV ... fluid into the interstitium ... pulmonary disease and causes ... #Diagnosis #Radiology ... #CHF #CXR #Features
Autoimmune Myositis - Differential Diagnosis Framework

Inflammatory Myopathies: Commonly symmetric proximal muscle weakness, no substantial muscle pain
Autoimmune Myositis ... aspiration > 50% of pts ... statins - probably caused ... weakness • Severe cardiac ... Myositis #Myopathy #rheumatology