11 results
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... head and neck, pancreas ... biliary, renal, lung ... concentration PET-CT ... #diagnosis #management
Nontuberculous Mycobacteria (NTM) Infections 

Mycobacterial species other than those belonging to the Mycobacterium tuberculosis complex and
Milk • Food products ... fortuitum can produce ... lung disease, adenitis ... Hematologic malignancy ... Imaging, high res CT
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
• Chronic lung ... lymphocytic interstitial lung ... Chest CT: • Ground-glass ... hypogammaglobulinemia #immunology #hematology ... #diagnosis #management
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
highly inflammatory disease ... rash) • Heart, lung ... Fibrin degradation products ... Syndrome #Diagnosis #Management ... #Hematology #Rheumatology
Nutrition in Cirrhosis: Dos and Don’ts
Screening:
 • Patients at risk for RFH-Nutritional Prioritizing Tool
 • Low
Anthropometry, CT ... pattern (avoiding long ... detrimental effect of long ... Cirrhosis #diet #management ... #hepatology #pathophysiology
Blood Product Transfusions One Pager Summary
Type and screen - determines blood type and detects in recipient
Related Acute Lung ... Graft Versus Host Disease ... Borrellia (Lyme disease ... Transfusions #diagnosis #management ... #hematology #reactions
Fungal Biomarkers: Beta-D-Glucan and Aspergillus Galactomannan
Beta-D-Glucan:
 • Polysaccharide cell wall component of many fungi
 • Pathogens:
infection (IFI) in hematologic ... or other blood products ... colonization vs invasive disease ... Clav (may be + as long ... Galactomannan #diagnosis #comparison
Scleroderma Like Conditions - Differential Diagnosis
Eosinophilic Fasciitis:
 - Orange peel induration (peau d'orange) of proximal extremities
patients with kidney disease ... Typically seen in long-standing ... Exposure: - Can produce ... Differential #Diagnosis #comparison ... #table #dermatology
Blood Transfusion Reactions

Immune Mediated:
 • Febrile Non-Hemolytic Transfusion Reaction (FNHTR): Most common immune reaction to transfusion.
Related Acute Lung ... Blood products contain ... of transfused products ... Transfusion #diagnosis #management ... #hematology #reactions
Performance Characteristics for Colorectal Cancer Screening Tests
Stool/blood-based tests:
 • FIT: 79% sensitivity, 94% specificity for CRC
rate for CRC, Long ... mortality 26% • CT ... Gastroenterology and Hepatology ... Screening #Tests #comparison ... #table #management