7 results
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
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IgG4-Related Disease ... Clinical history ... , biliary, renal ... concentration PET-CT ... 40% supporting long-term
Plain radiography of the abdomen revealed calcification of both adrenal glands. A homozygous mutation in LIPA
confirmed the diagnosis ... deficiency, or Wolman’s disease ... #clincial #peds ... #infant #NEJM # ... Wolmans #radiology #xray
Lichen Planus- ...On examination, numerous purple papules were noted on the anterior surface of the forearms
confirming the diagnosis ... an autoimmune disease ... used in primary treatment ... #NEJM #clinical ... #derm #wickhams
Broncholithiasis - Differential Diagnosis Framework

 • Also known as: Lung stones, pulmoliths, pneumoliths, bronchial calculi
 •
Also known as: Lung ... Broncholithiasis - Clinical ... : • Chest Xray ... bronchus • Chest CT ... Tracheobronchial Diseases
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
salivary and lacrimal glands ... Sjogren's Syndrome Diagnosis ... salivary ducts Clinical ... MALT Lymphoma • Lung ... Adenocarcinoma Treatment
Squamous-Cell Carcinoma of the Lung- ...Physical examination revealed decreased air entry in the base of the
Carcinoma of the Lung ... biopsy confirmed a diagnosis ... indicated stage IV disease ... #NEJM #clinical ... #radiology #CT #
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
Violaceous papules or plaques ... auricular papules Clinical ... had more severe disease ... Non-small-cell lung ... positive patients Treatment