8 results
Plain radiography of the abdomen revealed calcification of both adrenal glands. A homozygous mutation in LIPA
glands. ... deficiency, or Wolman’s disease ... #clincial #peds ... #infant #NEJM # ... Wolmans #radiology #xray
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... Clinical history ... concentration PET-CT ... 40% supporting long-term ... IgG4 #Related #Disease
Extramammary Paget’s Disease - The physical examination revealed an erythematous velvety plaque with superficial white scale
Extramammary Paget’s Disease ... erythematous velvety plaque ... cells (Panel B) #Clinical ... #Derm #Honc #Extramammary ... ExtramammaryPaget #NEJM
Lichen Planus- ...On examination, numerous purple papules were noted on the anterior surface of the forearms
Lichen Planus- . ... an autoimmune disease ... used in primary treatment ... #NEJM #clinical ... #derm #wickhams
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
multisystemic disease ... associated with other diseases ... demyelinating disease ... peripheral Thyroid Disease ... Tracheobronchial disease
Broncholithiasis - Differential Diagnosis Framework

 • Also known as: Lung stones, pulmoliths, pneumoliths, bronchial calculi
 •
Also known as: Lung ... Broncholithiasis - Clinical ... Diagnosis: • Chest Xray ... bronchus • Chest CT ... Tracheobronchial Diseases
Squamous-Cell Carcinoma of the Lung- ...Physical examination revealed decreased air entry in the base of the
Carcinoma of the Lung ... base of the right lung ... indicated stage IV disease ... #NEJM #clinical ... #radiology #CT #
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
Violaceous papules or plaques ... auricular papules Clinical ... had more severe disease ... Non-small-cell lung ... positive patients Treatment