9 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... meningitis), MCC CNS symptoms ... inhibitors • Uveitis- Ophthalmology ... #diagnosis #management ... #signs #symptoms
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: • Behçet Syndrome ... ulcers, cutaneous, ocular ... • Cogan Syndrome ... : - Ocular inflammatory ... Presentation - Systemic Symptoms
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Presentation: Systemic Symptoms ... • Progressive symptoms ... • Behcet syndrome ... • Cogan syndrome ... : Ocular inflammatory
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
systemic inflammatory vasculitis ... required due to skip ... required +/- prompt ophthalmology ... Temporal #Signs #Symptoms ... #Diagnosis #Management
Rheumatoid Arthritis - Signs and Symptoms
 • Ocular: Keratoconjunctivitis sicca, Episcleritis, Scleritis, Scleromalacia perforans
 • Pulmonary:
Rheumatoid Arthritis ... • Ocular: Keratoconjunctivitis ... Complications of DMARDs • Skin ... Vascular: Rheumatoid vasculitis ... Thrombocytosis, Felty's syndrome
Adult Onset Still's Disease
Systemic inflammation with urticarial rash.
Rash: 
 • Nonpruritic, evanescent (correlates with time of
the chest/trunk Symptoms ... A nonpruritic macular ... maculopapular skin ... Stills #disease #AOSD ... #rheumatology #management
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Cryofibrinogenemia Symptoms ... malignancies, vasculitis ... pulmonary emboli, and ocular ... to medium-sized arteries ... Antiphospholipid syndrome
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
3rd Decade Skin ... Erythematous, macular ... ANCA-associated vasculitis ... Seizures • Strokes Skin ... Induced Lupus: • Symptoms
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
gland) biopsy • Ocular ... ) • Cutaneous vasculitis ... : 2% Systemic Vasculitis ... Arthralgia and Arthritis ... Rheumatology #Diagnosis #Management