4 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... coronary artery aneurysms ... : Giant retinal ... Glucocorticoids 5-ASA ... #management #signs
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
VASCULITIS: • Behçet ... Thrombosis and arterial aneurysms ... diminished, or tender pulses ... aneurysm • Medium ... LFT • ESR • ANA
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
< 30 years • Aorta ... claudication, pulse ... Arteritis): • Aorta ... vasculitis • Behcet ... Thrombosis and arterial aneurysms
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
chondritis • Ocular ... Large vessels (aorta ... other large vessel aneurysms ... Sarcoidosis • Behcet ... #management