7 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... white matter, spinal ... inhibitors • Uveitis- Ophthalmology ... #management #signs ... #symptoms #rheumatology
Blurry Vision - Differential Diagnosis Framework

Anatomical Approach to Eye Disease:
1. Lids/Lashes
2. Extraocular Muscles/Motility
3. Conjunctiva/Sclera
4. Cornea
5. Anterior
Approach to Eye Disease ... Anterior Chamber ... Ocular Adverse Effects ... • Sjögren’s syndrome ... differential #diagnosis #ophthalmology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
GPA Cutaneous Single ... Vasculitis: • Behcet ... Disease • Cogan ... syndrome #Cutaneous ... #dermatology #rheumatology
Optic Neuritis - Diagnosis and Management
 • Epidemiology: Female (75%), 18-50 years,
caucasian
 • Symptoms: Moderate visual
Unilateral • Signs ... : RAPD (Marcus Gunn ... MRI: ON- focal, anterior ... other auto-immune diseases ... #ophthalmology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
, and ocular inflammation ... VASCULITIS: • Behçet ... • Cogan Syndrome ... purpura: strong sign ... differential #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
purpura: Strong sign ... vasculitis • Behcet ... syndrome: Recurrent ... : Ocular inflammatory ... Differential #Diagnosis #Rheumatology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
involvement: May involve anterior ... skeleton-sacroiliac joint and spine ... sites such as the collar ... osteoarticular and skin disease ... #Rheumatology #