3 results
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
accumulation of clinical ... , ↓ Fibrinogen level ... Infections+++: Virus (EBV ... biologics (CMV +++, EBV ... of emergency, ICU
Cullen's sign. Lipase 1,781. Bruising in the skin around the umbilicus. This sign is named after
Clinical Significance ... a significant clinical ... Diagnosis and Context ... #cullensign #em ... peritonitis #IM #FM #ICU
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
some ethnicities (e.g ... populations) CLINICAL ... Birbeck granules (EM ... DIAGNOSIS • Imaging ... Histiocytosis #Diagnosis