4 results
Systemic Sclerosis Associated Autoantibodies
Anti-topoisomerase I (anti-Sc170): Diffuse skin disease, Pulmonary fibrosis
Anti-centromere: Limited skin disease (~93-95%), Pulmonary
Systemic Sclerosis ... hypertension, Digital ulcers ... , Primary Biliary ... BCM_InternalMed #Systemic ... Autoantibodies #diagnosis #rheumatology
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
Systemic Sclerosis ... Scleroderma) Multi-system ... Hepatic: PBC (primary ... Raynaud's, digital ulcers ... Scleroderma #SSc #rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Primary (essential ... processes: • Systemic ... sensitivity • Painful ulcers ... Cryofibrinogenemia #diagnosis #rheumatology ... #hematology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
with GCA or as primary ... livedo reticularis, ulcers ... Rash, arthritis Primary ... genital aphthous ulcers ... Differential #Diagnosis #Rheumatology