20 results
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
Guillain-Barre Syndrome ... Clinical Features ... • Weakness: Starts ... axonal form • MRI ... management #treatment #neurology
Criss-Cross Gait on Physical Exam 

Seen in Glucose Transporter type 1 Deficiency Syndrome

#CrissCross #Criss #Cross #Gait
Syndrome #CrissCross ... #Cross #Gait #PhysicalExam ... #clinical #video ... #neurology #GLUT1 ... #deficiency
Causes of Neuromuscular Weakness
 • Spinal Cord: Demyelinating Disease (MS), Epidural abscess, Infarction, Syringomyelia, Tetanus, Transverse
Poliomyelitis, Guillain-Barre ... syndrome, Mononeuritis ... heavy metals), Critical ... : Acid maltase deficiency ... differential #diagnosis #neurology
Locked-In Syndrome on Physical Exam

56 year-old male with acute onset altered sensorium. Suffered a cardiac arrest
Locked-In Syndrome ... infarct seen on MRI ... #PhysicalExam # ... clinical #video ... #neurology
Guillain-Barré Syndrome (GBS)
Acute autoimmune demyelinating polyradiculoneuropathy that presents with rapidly progressive flaccid weakness
Epidemiology:
 • Incidence: 1
Guillain-Barré Syndrome ... transplantation CLINICAL ... - Spinal MRI may ... #Syndrome #diagnosis ... #management #neurology
Leigh Syndrome 
History: 19-month-old girl with hypotonia, developmental 
delay, failure to thrive, and bilateral optic disc
Leigh Syndrome ... was a complex I deficiency ... MarkMamloukMD #Leigh #Syndrome ... #Clinical #MRI ... Brain #Diagnosis #Radiology
Imaging Patterns of Toxic and Metabolic Brain Disorders

Thalami, Mammillary Bodies and Tectum: Wernicke Encephalopathy
Dentate Nuclei: Metronidazole,
Encephalopathy, Cobalamin Deficiency ... Pons: ODS #MRI ... Brain #Disorders #Clinical ... Differential #Diagnosis #Radiology ... #Neurology
Man in the Barrel Syndrome on Physical Exam
Bilateral brachial paresis, mainly proximal, with preserved motor function
Man in the Barrel ... #Man #Barrel #Syndrome ... #PhysicalExam # ... clinical #video ... #neurology
Leg Asterixis on Physical Exam

Asterixis can be seen in peripheral neuropathies also! Check out this leg
occurring in Guillain Barre ... syndrome. ... Leg #Asterixis #PhysicalExam ... #clinical #neurology
One and a Half Syndrome on Physical Exam

This 28 year old patient presented to clinic with
One and a Half Syndrome ... MRI was ordered ... diagnosed with MS, and started ... #PhysicalExam # ... ophthalmology #neurology