29 results
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
Metabolism A table ... IEM schema for supplemental ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... Peds #Pediatrics #Table
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
the lab values table ... for supplemental ... Pathophysiology #Diagnosis #Algorithm ... Peds #Pediatrics #Table
Central distribution is seen in sarcoidosis and cardiogenic pulmonary edema.
Peripheral distribution is mainly seen in cryptogenic
#Diagnosis #Radiology ... #Pulmonary #HRCT ... #Differential #Table
Upper lung zone preference is seen in:
- Inhaled particles: pneumoconiosis (silica or coal)
- Smoking related diseases
edema #Diagnosis #Radiology ... #Pulmonary #HRCT ... #Differential #Table
Differential diagnosis on HRCT
Most of our knowledge about imaging findings in interstitial lung disease comes from
Differential diagnosis on HRCT ... disease comes from HRCT ... On HRCT there are ... low attenuation (table ... #Diagnosis #Radiology
Low Attenuation pattern 
1. Lymphangiomyomatosis (LAM): uniform cysts in woman of child-bearing age; no history of
#Clinical #Radiology ... #HRCT #CTChest ... Pattern #Comparison #Table
Nodular pattern
1. Hypersensitivity pneumonitis: ill defined centrilobular nodules.
2. Miliary TB: random nodules
3. Sarcoidosis: nodules with perilymphatic
#Clinical #Radiology ... #HRCT #CTChest ... Pattern #Comparison #Table
High Attenuation pattern 
1. Chronic eosinophilic pneumonia with peripheral areas of ground glass opacity.
2. Sarcoid end-stage
consolidation #Clinical #Radiology ... #HRCT #CTChest ... Pattern #Comparison #Table
Nodular pattern(2)
1. Sarcoidosis: nodules with perilymphatic distribution, along fissures, adenopathy.
2. TB: Tree-in-bud appearance in a patient
#Clinical #Radiology ... #HRCT #CTChest ... Pattern #Comparison #Table
High Attenuation pattern (2) 
1. Non specific interstitial pneumonitis (NSIP): ground glass with traction bronchiectasis, no
#Clinical #Radiology ... #HRCT #CTChest ... Pattern #Comparison #Table