5 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
vasculitis) • ... skin injury) • Neurologic ... disease (SVC/IVC occlusion ... tears, Ischemia, ... inhibitors • Uveitis- Ophthalmology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... : • Behçet Syndrome ... • Cogan Syndrome ... well as inner ear ... reactions, and vaso-occlusive
One and a Half Syndrome on Physical Exam

This 28 year old patient presented to clinic with
One and a Half Syndrome ... the follow up video ... the hospital, diagnosed ... #ophthalmology ... #neurology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis Framework ... pulmonary and renal ... reactions, and vaso-occlusive ... affects the skin, neurologic ... cognitive impairment, neurologic
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... pulmonary emboli, and ocular ... thrombi including retinal ... and/or venous occlusions ... Antiphospholipid syndrome