2 results
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... Diastolic dysfunction ... pulmonary Langerhans cell ... Others: tumoral ... #Differential #Causes
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
LCH is a rare disorder ... : LCH exhibits features ... commonly in the skull ... • Endocrine Dysfunction ... marrow: Organ dysfunction