11 results
Autoimmune Hepatitis

Clinical Presentation
 - Highly variable clinical presentation, from subclinical disease to acute liver failure.
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Autoimmune Hepatitis ... , AIH diagnosis ... Hepatitis (eg Viral) Management ... BryanCUlrich #Autoimmune ... #Management #Hepatology
Erythemas Summarized
Erythema ab igne
 • A dermatosis that results from repeated exposure to heat (fires, heating
Summarized Erythema ab ... malignancies, autoimmune ... PrathitKulkarni #Erythemas #comparison ... #differential #diagnosis ... #dermatology #compared
Adult-Onset Still's Disease (AOSD)
Rare inflammatory disorder of unknown etiology, difficult to diagnose because of heterogenous presentation.
, difficult to diagnose ... likely conditions (autoimmune ... maculopapular rash ... Disease #AOSD #rheumatology ... #diagnosis #management
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
Differential Diagnosis ... disease • Non-autoimmune ... Malignancy (e.g. hematologic ... deficiencies • Autoimmune ... Erythematosus #Diagnosis
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
50,000 patients • Avg ... : Pneumonia • Autoimmune ... and M panel Management ... hypogammaglobulinemia #immunology #hematology ... #diagnosis #management
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
NPSLE rare, Malar rash ... Manifestations: Malar rash ... druginduced #lupus #sle #comparison ... #table #rheumatology ... #diagnosis #management
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
be any age) Autoimmune ... Sjogren's Syndrome Diagnosis ... RTA, TYPE I RTA Diagnosis ... Nephrogenic DI Hematologic ... #Diagnosis #Management
Blood Transfusion Reactions

Immune Mediated:
 • Febrile Non-Hemolytic Transfusion Reaction (FNHTR): Most common immune reaction to transfusion.
antigens (often ABO ... maculopapular rash ... anti-HLA or anti-HNA Ab ... #Transfusion #diagnosis ... #management #hematology
Blood Product Transfusions One Pager Summary
Type and screen - determines blood type and detects in recipient
antigens (often ABO ... maculopapular rash ... anti-HLA or anti-HNA Ab ... #Transfusions #diagnosis ... #management #hematology
Autoimmune Myositis - Differential Diagnosis Framework

Inflammatory Myopathies: Commonly symmetric proximal muscle weakness, no substantial muscle pain
- Differential Diagnosis ... myopathies Diagnostic ... Symptoms: • Gottron rash ... Anti-Synthetase Ab ... Myositis #Myopathy #rheumatology