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2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
Polyangiitis (GPA ... Polyangiitis (MPA ... #Polyangiitis #GPA ... Management #rheumatology ... #algorithm #vasculitis
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Cell Arteritis (GCA ... Polyangiitis (GPA ... (MPA) • Eosinophilic ... Sources: GCA ... #rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (GPA ... Polyangiitis (MPA ... #Polyangiitis #GPA ... #MPA #ANCA #Vasculitis ... #rheumatology
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Post-strep GN, Lupus ... ANCA (C-ANCA): GPA ... >>> MPA > eGPA ... GPA Stanford Internal ... #rheumatology
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
polyangiitis (GPA ... ), microscopic polyangiitis ... (MPA), and eosinophilic ... Microscopic polyangiitis ... PR3 #Diagnosis #Rheumatology
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... inflammation: • Microscopic ... polyangiitis (GPA ... differential #diagnosis #algorithm ... #rheumatology
Inflammatory Joint Pain - Differential Diagnosis Algorithm 
Monoarticular
 • Gout (Podagra, Tophi)
 • Pseudogout
 • Early
Differential Diagnosis Algorithm ... Arthritis • Systemic Lupus ... polyangiitis (GPA ... )/microscopic polyangiitis ... (MPA) Insidious
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
> PR3 60% • GPA ... and branches • GCA ... • ANCA (Dx: GPA ... , EGPA, microscopic ... differential #diagnosis #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Associated: - Microscopic ... polyangiitis - EGPA ... - GPA Cutaneous ... #skin #dermatology ... #rheumatology #
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Associated with Joint ... Sarcoidosis • GPA ... lesions • Discoid lupus ... #joint #pain #skin ... differential #diagnosis #rheumatology