3 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
enzyme, X-linked, Autoinflammatory ... Clinical Syndrome ... : • Common Clinical ... polyarteritis nodosa (12% ... myeloid cells NEJM
Plain radiography of the abdomen revealed calcification of both adrenal glands. A homozygous mutation in LIPA
acid lipase is critical ... of cholesteryl esters ... #clincial #peds ... calcifications #infant #NEJM ... #Wolmans #radiology
Hypertensive Disorders of Pregnancy
Chronic Hypertension:
 • Guidelines as SBP ≥130 or DBP ≥ 90 mmHg
 •
and persists > 12 ... before Anti-HTN meds ... patients • HELLP: Syndrome ... ↑ in anti HTN meds ... diagnosis so have high clinical