4 results
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
< 30 years - Aorta ... : - Aorta and ... Thrombosis and arterial aneurysms ... aortitis, aortic aneurysm ... differential #diagnosis #rheumatology
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
systemic inflammatory vasculitis ... those coming off aorta ... in literature (NEJM ... cases (Cornelia NEJM ... them, but urgent rheumatology
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Retroperitoneum and aorta ... concentration PET-CT ... conventional imaging (aorta ... No necrosis, No vasculitis ... workup #treatment #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
< 30 years • Aorta ... Elevated ESR and CRP GCA ... Arteritis): • Aorta ... Thrombosis and arterial aneurysms ... Differential #Diagnosis #Rheumatology