4 results
Portopulmonary Hypertension
Presence of pulmonary arterial hypertension in a patient with portal hypertension
No other obvious causes (chronic
causes (chronic lung ... disease, left heart ... disease, thromboembolism ... Transthoracic echocardiogram ... #diagnosis #management
Chronic Thromboembolic Pulmonary Hypertension (CTEPH) and Pulmonary Thromboendarterectomy
Chronic Thromboembolic Pulmonary Hypertension
Definition: mean pulmonary-artery pressure > 25mmHg
Thromboembolic Pulmonary Hypertension ... Plexiform-lesion formation Clinical ... Ventilation-perfusion lung ... have inoperable disease ... Thromboendarterectomy #diagnosis #management
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Fever is the main clinical ... rash) • Heart, lung ... thrombocytopenia • Liver function ... Syndrome #Diagnosis #Management ... #Hematology #Rheumatology
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
auricular papules Clinical ... had more severe disease ... and diminished functional ... Dermatomyositis #diagnosis #management ... #rheumatology #