4 results
Polycythemia Vera (PV) - Diagnosis and Management Summary
Diagnostic Criteria:
 • Elevated hemoglobin and/or hematocrit AND
 •
Management Summary ... for PV are not ... • Treatment algorithms ... #Summary #treatment ... #hematology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Auto-amplification loop Diagnosis ... adenopathies, confusion ... Unknown cause Treatment ... #management #treatment ... #summary #rheumatology
Essential Thrombocythemia (ET)
ET is a chronic myeloproliferative neoplasm. Most cases are related to mutations that affect
Splenomegaly Diagnosis ... A conclusive diagnosis ... PV, MDS, CML) Treatment ... • Treatment algorithms ... #hematology
Pseudogout Summary - Calcium Pyrophosphate Deposition Disease (CPPD)

Pathophysiology:
Pyrophosphate produced by chondrocytes likely precipitates with calcium to
Pseudogout Summary ... after surgery/trauma ... Acute Pseudogout: Treatment ... Syndrome: • A rare ... Deposition #Disease #Rheumatology