2 results
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Goodpasture's cause ... hemorrhage (DAH) • Diffuse ... sparing of the lung ... • IF staining patterns ... differential #diagnosis #management
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
for bone, skin, lungs ... Incidence: 4–5 cases ... Birbeck granules (EM ... therapies for cases ... Histiocytosis #Diagnosis #Management