74 results
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
schema of the pathophysiology ... inborn errors of metabolism ... connections and pathophysiology ... of information: Pediatrics ... , UpToDate #Pediatrics
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
Inborn Errors of Metabolism ... from UpToDate and Pediatrics ... diagnosing acute metabolic ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... Neonatology #Peds #Pediatrics
Metformin Associated Lactic Acidosis (MALA) 

Pathophysiology of MALA
 - Metformin interferes with the activity of the
Associated Lactic Acidosis ... (MALA) Pathophysiology ... use in cellular metabolism ... acidosis including ... Toxicology #Diagnosis #Management
Tetralogy of Fallot Summary
 • Anatomy
 • Incidence
 • Pathophysiology
 • Presentation
 • Common Variants
 •
• Incidence • Pathophysiology ... palliation • Post-Op Management ... Fallot #diagnosis #management ... #cardiology #peds ... #pediatrics #treatment
Aortic Stenosis & Bicuspid Aortic Valve (AS)
 • Introduction & Pathophysiology
 • Classifications
 • Epidemiology
 •
Introduction & Pathophysiology ... Pre-operative Management ... Post-operative Management ... #AorticValve #cardiology ... #peds #pediatrics
Atrioventricular Septal Defect
aka AV canal defect aka endocardial cushion defect
 • Epidemiology and Associations
 • Embryology
Physical Exam • Pathophysiology ... Post-Operative ICU Management ... cushion #diagnosis #management ... #peds #pediatrics ... #cardiology
Tetralogy of Fallot - Hypoxic Spell Management
1. Oxygenation
2. Increase SVR
3. Abolish Hyperpnea
4. Correct Acidosis

- Dr. Rasha
Hypoxic Spell Management ... Correct Acidosis ... Hypoxic #Spell #Management ... #Peds #Pediatrics
Truncus Arteriosus
 • Basic Information
 • Embryology
 • Associated anomalies
 • Pathophysiology/Presentation
 • Pre-operative management
 •
anomalies • Pathophysiology ... Pre-operative management ... Outcomes • Post-op management ... #cardiology #peds ... #pediatrics
Ebstein Anomaly
 • Prevalence
 • Pathophysiology
 • Presentation
 • Physical Examination Findings
 • Initial Management
 •
Prevalence • Pathophysiology ... Findings • Initial Management ... Anomaly #diagnosis #management ... #cardiology #pediatrics
Total Anomalous Pulmonary Venous Return (TAPVR)
 • Introduction
 • Classification
 • Pathophysiology of TAPVR
 • Presentation
Classification • Pathophysiology ... Pre-Operative Management ... Post-Operative Management ... #cardiology #peds ... #pediatrics #summary