250 results
Gitelman Syndrome Overview

What?
• Inherited (AR) hypokalemic salt-losing tubulopathies affecting the thiazide-sensitive sodium chloride cotransporter
• Gitelman's syndrome
tubule (DCT) Clinical ... Hypocalciuria (spot urine ... ratio 0.5%) Differential ... Syndrome #diagnosis #nephrology ... #management #pathophysiology
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
schema of the pathophysiology ... inborn errors of metabolism ... connections and pathophysiology ... #Pediatrics #Metabolism ... Diagnosis #Algorithm #Differential
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
Inborn Errors of Metabolism ... diagnosing acute metabolic ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... #InbornErrors #Metabolism
Urine Electrolyte Interpretation - AKI, Hyponatremia, Hypokalemia and Non-Gap Metabolic Acidosis

#Urine #Electrolytes #Interpretation #ULytes #AKI #FENa
Urine Electrolyte ... Hypokalemia and Non-Gap Metabolic ... Acidosis #Urine ... #FENa #FEUrea #Nephrology
Primary Metabolic Alkalosis - Differential Diagnosis Algorithm
Volume Depleted 2° hyperaldosteronism
 • Low Urine Cl-: Vomiting, NGT
Primary Metabolic ... Alkalosis - Differential ... hyperaldosteronism • Low Urine ... (late) • High Urine ... Diagnosis #Algorithm #nephrology
Primary Metabolic Alkalosis - Differential Diagnosis Algorithm
Volume Depleted - 2° hyperaldosteronism
 • Low Urine Cl-: Vomiting,
Primary Metabolic ... Alkalosis - Differential ... hyperaldosteronism • Low Urine ... (late) • High Urine ... Diagnosis #Algorithm #Nephrology
High Anion Gap Metabolic Acidosis (HAGMA) - Differential Diagnosis - GOLDMARK

Glycols - ethylene and propylene glycol
Oxoproline
High Anion Gap Metabolic ... Acidosis (HAGMA) - Differential ... during hypoxic metabolism ... Acidosis #HAGMA #Differential ... GOLDMARK #mnemonic #nephrology
Purple Urine Bag Syndrome
Chronic, indwelling catheter + bacteriuria (Providencia, Klebsiella, E.coli*) + alkaline urine
Tryptophan → Indoxyl
Purple Urine Bag ... E.coli*) + alkaline urine ... Syndrome #PUBS #pathophysiology ... #clinical #photo ... #differential #
Metabolic Alkalosis - Urinary Chloride Algorithm
Cl- responsive metabolic alkalosis
 • Kidney loss of Cl-
LiCl use The urine ... Urine chloride is ... settings, the urine ... #Algorithm #nephrology ... #differential #
Metabolic Pathways of Purple Urine Bag Syndrome: Adopted from chart originally published in Purple Urine Bag
Metabolic Pathways ... of Purple Urine ... published in Purple Urine ... #Pathophysiology ... #PUBS #Purple #Urine