5 results
Plain radiography of the abdomen revealed calcification of both adrenal glands. A homozygous mutation in LIPA
glands. ... confirmed the diagnosis ... and gut, which causes ... #clincial #peds ... #infant #NEJM #
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Related Disease Clinical ... pancreas, biliary, renal ... aorta, salivary glands ... supporting long-term ... #rheumatology
Lichen Planus- ...On examination, numerous purple papules were noted on the anterior surface of the forearms
sawtooth rete pegs ... confirming the diagnosis ... used in primary treatment ... #NEJM #clinical ... #derm #wickhams
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
Violaceous papules or plaques ... auricular papules Clinical ... Muscle atrophy may cause ... positive patients Treatment ... #rheumatology #
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
salivary and lacrimal glands ... Hypocomplementemia • Can cause ... salivary ducts Clinical ... Adenocarcinoma Treatment ... Sjogrens #Syndrome #Rheumatology