8 results
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
, causes and management ... - French Vasculitis ... vasculitis Clinical ... with purpura - Renal ... neuropathy Treatment
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Identification of causes ... disease (10%) : SLE ... hemopathies (4%) • Cryoglobulinemia ... #dermpath #dermatology ... lesions #diagnosis #clinical
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
• They can cause ... Cryoglobulins Cause ... Syndrome: • Clinical ... (e.g. systemic lupus ... erythematosus (SLE
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
tract, and often causes ... ANCA +MPO) • Cryoglobulinemic ... inflammation Others: • Lupus ... such as systemic lupus ... , and SLE) • Urinalysis
Retinal Vasculitis in Takayasu’s Arteritis- ...Ophthalmologic examination revealed severe impairment, with perception of only light in
Retinal Vasculitis ... , large-vessel vasculitis ... and initiated treatment ... #NEJM #clinical ... #radiology #fluorescein
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... Cryofibrinogenemia Clinical ... thrombi including retinal ... Diagnosis: • + Clinical ... cryoglobulins • Negative causes
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
overlaps with RA, SLE ... Hypocomplementemia • Can cause ... salivary ducts Clinical ... : • 7%, Cryoglobulinemia ... Adenocarcinoma Treatment
Monoclonal Gammopathy of Renal Significance (MGRS)

MGRS
• MGRS refers to kidney disease caused by nephrotoxic monoclonal immunoglobulins
kidney disease caused ... Clinical Clues: ... formation causing vasculitis ... immunotactoid GN, cryoglobulinemic ... microangiopathy Treatment