21 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Somatic) Syndrome Clinical ... Syndrome: • Common Clinical ... Features: alveolitis, ear ... myeloid cells NEJM ... Autoinflammatory #Somatic #rheumatology
Intraoperative Massive Blood Loss - Guidelines for Crises in Anaesthesia
Expected or unexpected major haemorrhage

❶ Call for
inform theatre team ... equipment. ❽ Discuss management ... an appropriate clinical ... BloodLoss #Hemorrhage #Anesthesiology ... Checklist #Diagnosis #Management
Cardiac Tamponade - Guidelines for Crises in Anaesthesia
Caused by an accumulation of blood, pus, effusion fluid
help and inform clinical ... team of problem ... Plan definitive management ... Cardiac #Tamponade #Anesthesiology ... Checklist #Diagnosis #Management
Local Anaesthetic Toxicity - Guidelines for Crises in Anaesthesia
Signs of severe toxicity:
 • Sudden alteration in
inform immediate clinical ... team of problem ... Anaesthetic #Toxicity #Anesthesiology ... Checklist #Diagnosis #Management
Susac Syndrome - Clinical Triad
 - Central nervous system dysfunction
 - Branch retinal artery occlusion
 -
Susac Syndrome - Clinical ... disease flares - 2-year ... Triad #Diagnosis #Management ... #Rheumatology
Intraoperative Bronchospasm - Guidelines for Crises in Anaesthesia

❶ Call for help and inform theatre team of
inform theatre team ... Other drugs at clinician ... X-ray as soon as clinically ... anaesthesia #Anesthesiology ... Checklist #Diagnosis #Management
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
accumulation of clinical ... Assessment • Clinical ... Nicolas Taar ... Lymphohistiocytosis #diagnosis #management ... treatment #summary #rheumatology
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
Diagnosis = clinical ... in literature (NEJM ... cases (Cornelia NEJM ... them, but urgent rheumatology ... Symptoms #Diagnosis #Management
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... Behcet syndrome (Clinical ... Giant retinal tears ... Syndrome #diagnosis #management ... signs #symptoms #rheumatology
High Central Neuraxial Block - Guidelines for Crises in Anaesthesia
• Can occur with deliberate or accidental
hypnosis as soon as clinical ... inform theatre team ... Neuraxial #Block #Anesthesiology ... Checklist #Diagnosis #Management