Pleuroparenchymal Fibroelastosis (PPFE) on Chest CT 47 M with idiopathic pleuroparenchymal fibroelastosis. Typical imaging findings: - Upper lobe volume loss, distortion - Dense subpleural and pleural fibrosis - Rare - GVHD, lung transplant, radiation, drug, idiopathic Dr. Jeffrey Kanne @JeffreyKanneMD #Pleuroparenchymal #Fibroelastosis #PPFE #ChestCT #radiology #clinical #pulmonary #CXR