Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
• Recurrent, idiopathic oral ulcers with 2 3 episodes within a 12 month period AND
• Meeting ≥ 2 of the following 4 criteria:
- Recurrent genital ulcers
- Ocular disease: Uveitis or retinal vasculitis
- Skin lesions consistent with Behcet's
- Abnormal pathergy test
Most Common Clinical Features:
• Painful, oral and genital ulcers
• Wide variety of skin lesions (e.g. acneiform eruptions, pseudofolliculitis, erythema nodosum)
• Ocular disease (e.g. uveitis, retinal vasculitis)
• Arthritis (asymmetric, oligoarticular, medium-large joints)
• Vascular lesions (e.g. venous thromboses, arterial aneurysms)
Phenotypes of Behcet's: Ocular Behcet's, Intestinal Behcet's, Neuro-Behcet's, Mucocutaneous and articular, Parenchymal neurological and ocular, Extra-parenchymal neurological and peripheral vascular
- Dr. Eric Strong @DrEricStrong - Strong Medicine https://www.youtube.com/c/EricsMedi
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