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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
or proteinase 3 ... Presentation - Systemic Symptoms ... purpura: strong sign ... are proteinase 3 ... Cryoglobulins • HIV
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Vasculitis - Differential ... Presentation: Systemic Symptoms ... purpura: Strong sign ... • Progressive symptoms ... or proteinase 3
Rheumatoid Arthritis Summary
MCP and PIP Involvement, Spares DIP, Carpal Tunnel, Sicca Syndrome, Epi/Scleritis, Heart Disease, Rheumatoid
, Rheumatoid Vasculitis ... Rheumatoid Nodules, Pulmonary ... Disease and ILD ... #rheumatology #signs ... #symptoms
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
- HIV infection ... dysfunction 3. ... pulmonary disease ... obstructive pattern IV ... neurofibromatosis, vasculitis
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Butterfly rash, Vasculitis ... Aseptic necrosis of hip ... pain (20%) Renal disease ... erythematosus #signs ... #symptoms #diagnosis
Weakness - Differential Diagnosis Framework

Approach To Weakness:
 • Non-neuromuscular disorder (Cardiac, pulmonary etc)
 • CNS ->
disorder (Cardiac, pulmonary ... Inflammatory: Vasculitis ... multiplex (DM, Vasculitis-polyarteritis ... anti-Jo-1] - (Vasculitis ... dystrophies, or vasculitis
Neurological Manifestations of Tuberculosis
Spinal Arachnoiditis & Polyradiculopathy:
 • Subacute onset of limb weakness, bladder/bowel dysfunction, muscle
lesion Pott's Disease ... (IRIS): • In HIV ... lymphadenopathy, pulmonary ... Meningitis • Include: vasculitis ... Children with pulmonary
Rheumatoid arthritis (RA): Extra-articular manifestations
Skin: 
 • Inflammation of skin (esp. over areas of stress) forms
blood vessels (vasculitis ... interstitial lung disease ... /pulmonary fibrosis ... pathophysiology #signs ... #symptoms #diagnosis
Nontuberculous Mycobacteria (NTM) Infections 

Mycobacterial species other than those belonging to the Mycobacterium tuberculosis complex and
mucogenicum • HIV ... Hematologic malignancy 3. ... gastrointestinal symptoms ... • Clinical (Symptoms ... differential #diagnosis #infectiousdiseases
Rheumatoid Arthritis - Signs and Symptoms
 • Ocular: Keratoconjunctivitis sicca, Episcleritis, Scleritis, Scleromalacia perforans
 • Pulmonary:
Rheumatoid Arthritis - Signs ... and Symptoms • ... Scleromalacia perforans • Pulmonary ... Vascular: Rheumatoid vasculitis ... Arthritis #RA #Signs