3 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
VEXAS (Vacuoles, E1 ... Abnormalities: macrocytic anemia ... , thrombocytopenia ... (MDS) Most met criteria ... Autoinflammatory #Somatic #rheumatology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Macrophage Activation ... with leukopenia, anemia ... , and thrombocytopenia ... Histopathologic criteria ... #Rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
- Cytopenias (anemia ... , thrombocytopenia ... Diagnostic Criteria ... of 8 HLH-2004 criteria ... Diagnosis #Management #Hematology