7 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
(panuveitis, retinal ... to local skin injury ... is a skin prick test ... Recurrent and chronic ... Glucocorticoids 5-ASA
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Syndromes (PRS) ... life-threatening diseases ... Inflammatory eye disease ... injury), Coags ... anti-GBM) Other tests
Bronchiectasis - Summary

What?
• Bronchiectasis is derived from the Greek words bronckos meaning airway and ectasis meaning
bronchial wall injury ... Connective tissue diseases ... • Mounier-Kuhn syndrome ... parenchyma Diagnosis ... Laboratory: • ANA
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... Eosinophilia, asthma, chronic ... • Cogan Syndrome ... retinopathy Lab Tests ... LFT • ESR • ANA
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Bronchiectasis, Chronic ... the extent of disease ... Manifestations: Renal ... : • Nephrotic syndrome ... Carpal tunnel syndrome
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
Differential Diagnosis ... • May involve PNS ... APLA/LAC: • Renal ... with Lupus: • Chronic ... Erythematosus #Diagnosis
Autoimmune Myositis - Differential Diagnosis Framework

Inflammatory Myopathies: Commonly symmetric proximal muscle weakness, no substantial muscle pain
- Differential Diagnosis ... Tests: • Measure ... aspiration > 50% of pts ... ANTI-MITOCHONDRIAL MYOPATHY: • Chronic ... muscular atrophy • Chronic