4 results
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... and renal manifestations ... : - ANCA-positive ... IgA-associated vasculitis, Behcet ... , anti-GBM ab, ANA
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... Syndromes and Mimics ... - Differential ... Disease - Double Positive ... IgA Vasculitis, Behcet's
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
disease (panuveitis, retinal ... Skin lesions • Positive ... disease) Differential ... Glucocorticoids 5-ASA ... azathioprine #Behcet
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential ... and renal abnormalities ... VASCULITIS: • Behçet ... Eye -> retinopathy ... LFT • ESR • ANA